PDB entry 1ptz
View 1ptz on RCSB PDB site
Description: Crystal structure of the human CU, Zn Superoxide Dismutase, Familial Amyotrophic Lateral Sclerosis (FALS) Mutant H43R
Class: oxidoreductase
Keywords: sod, fals mutant, amyotrophic lateral sclerosis, oxidoreductase
Deposited on
2003-06-23, released
2003-09-09
The last revision prior to the SCOPe 2.08 freeze date was dated
2009-02-24, with a file datestamp of
2009-03-01.
Experiment type: XRAY
Resolution: 1.8 Å
R-factor: 0.186
AEROSPACI score: 0.52
(click here for full SPACI score report)
Chains and heterogens:
- Chain 'A':
Compound: Superoxide dismutase [Cu-Zn]
Species: Homo sapiens [TaxId:9606]
Gene: SOD1
Database cross-references and differences (RAF-indexed):
- Uniprot P00441 (0-152)
- engineered (5)
- engineered (42)
- engineered (110)
Domains in SCOPe 2.08: d1ptza_ - Chain 'B':
Compound: Superoxide dismutase [Cu-Zn]
Species: Homo sapiens [TaxId:9606]
Gene: SOD1
Database cross-references and differences (RAF-indexed):
- Uniprot P00441 (0-152)
- engineered (5)
- engineered (42)
- engineered (110)
Domains in SCOPe 2.08: d1ptzb_ - Heterogens: CU1, ZN, SO4, HOH
PDB Chain Sequences:
- Chain 'A':
Sequence; same for both SEQRES and ATOM records: (download)
>1ptzA (A:)
atkavavlkgdgpvqgiinfeqkesngpvkvwgsikglteglrgfhvhefgdntagctsa
gphfnplsrkhggpkdeerhvgdlgnvtadkdgvadvsiedsvislsgdhsiigrtlvvh
ekaddlgkggneestktgnagsrlacgvigiaq
- Chain 'B':
Sequence; same for both SEQRES and ATOM records: (download)
>1ptzB (B:)
atkavavlkgdgpvqgiinfeqkesngpvkvwgsikglteglrgfhvhefgdntagctsa
gphfnplsrkhggpkdeerhvgdlgnvtadkdgvadvsiedsvislsgdhsiigrtlvvh
ekaddlgkggneestktgnagsrlacgvigiaq