PDB entry 3t3j

View 3t3j on RCSB PDB site
Description: 1.70 A structure of Friedreich's ataxia frataxin variant N146K
Class: oxidoreductase
Keywords: Fe-S Cluster Biosynthesis, Human mitochondria, OXIDOREDUCTASE
Deposited on 2011-07-25, released 2011-08-10
The last revision prior to the SCOPe 2.03 freeze date was dated 2011-08-31, with a file datestamp of 2011-08-26.
Experiment type: XRAY
Resolution: 1.7 Å
R-factor: 0.214
AEROSPACI score: 0.52 (click here for full SPACI score report)

Chains and heterogens:

  • Chain 'A':
    Compound: Frataxin, mitochondrial
    Species: Homo sapiens [TaxId:9606]
    Gene: FXN, FRDA, X25
    Database cross-references and differences (RAF-indexed):
    • Uniprot Q16595
      • engineered mutation (64)
    Domains in SCOPe 2.03: d3t3ja_
  • Heterogens: HOH

PDB Chain Sequences:

  • Chain 'A':
    Sequence, based on SEQRES records: (download)
    >3t3jA (A:)
    gtlghpgsldettyerlaeetldslaeffedladkpytfedydvsfgsgvltvklggdlg
    tyvikkqtpnkqiwlsspssgpkrydwtgknwvyshdgvslhellaaeltkalktkldls
    slaysgkda
    

    Sequence, based on observed residues (ATOM records): (download)
    >3t3jA (A:)
    hpgsldettyerlaeetldslaeffedladkpytfedydvsfgsgvltvklggdlgtyvi
    kkqtpnkqiwlsspssgpkrydwtgknwvyshdgvslhellaaeltkalktkldlsslay
    sgk