PDB entry 3gw3

View 3gw3 on RCSB PDB site
Description: human UROD mutant K297N
Class: lyase
Keywords: uroporphyrinogen, decarboxylase, lyase, heme biosynthesis, porphyria, Disease mutation, Phosphoprotein, Porphyrin biosynthesis
Deposited on 2009-03-31, released 2009-07-07
The last revision prior to the SCOPe 2.08 freeze date was dated 2017-11-01, with a file datestamp of 2017-10-27.
Experiment type: XRAY
Resolution: 1.7 Å
R-factor: N/A
AEROSPACI score: 0.4 (click here for full SPACI score report)

Chains and heterogens:

  • Chain 'A':
    Compound: Uroporphyrinogen decarboxylase
    Species: Homo sapiens [TaxId:9606]
    Gene: UROD
    Database cross-references and differences (RAF-indexed):
    • Uniprot P06132
      • engineered (296)
    Domains in SCOPe 2.08: d3gw3a_
  • Heterogens: HOH

PDB Chain Sequences:

  • Chain 'A':
    Sequence, based on SEQRES records: (download)
    >3gw3A (A:)
    meanglgpqgfpelkndtflraawgeetdytpvwcmrqagrylpefretraaqdffstcr
    speacceltlqplrrfpldaaiifsdilvvpqalgmevtmvpgkgpsfpeplreeqdler
    lrdpevvaselgyvfqaitltrqrlagrvpligfagapwtlmtymvegggsstmaqakrw
    lyqrpqashqllriltdalvpylvgqvvagaqalqlfeshaghlgpqlfnkfalpyirdv
    akqvkarlreaglapvpmiifakdghfaleelaqagyevvgldwtvapkkarecvgntvt
    lqgnldpcalyaseeeigqlvkqmlddfgphryianlghglypdmdpehvgafvdavhkh
    srllrqn
    

    Sequence, based on observed residues (ATOM records): (download)
    >3gw3A (A:)
    gfpelkndtflraawgeetdytpvwcmrqagrylpefretraaqdffstcrspeaccelt
    lqplrrfpldaaiifsdilvvpqalgmevtmvpgkgpsfpeplreeqdlerlrdpevvas
    elgyvfqaitltrqrlagrvpligfagapwtlmtymvegggsstmaqakrwlyqrpqash
    qllriltdalvpylvgqvvagaqalqlfeshaghlgpqlfnkfalpyirdvakqvkarlr
    eaglapvpmiifakdghfaleelaqagyevvgldwtvapkkarecvgntvtlqgnldpca
    lyaseeeigqlvkqmlddfgphryianlghglypdmdpehvgafvdavhkhsrllrq