PDB entry 3gw3
View 3gw3 on RCSB PDB site
Description: human UROD mutant K297N
Class: lyase
Keywords: uroporphyrinogen, decarboxylase, lyase, heme biosynthesis, porphyria, Disease mutation, Phosphoprotein, Porphyrin biosynthesis
Deposited on
2009-03-31, released
2009-07-07
The last revision prior to the SCOPe 2.08 freeze date was dated
2017-11-01, with a file datestamp of
2017-10-27.
Experiment type: XRAY
Resolution: 1.7 Å
R-factor: N/A
AEROSPACI score: 0.4
(click here for full SPACI score report)
Chains and heterogens:
- Chain 'A':
Compound: Uroporphyrinogen decarboxylase
Species: Homo sapiens [TaxId:9606]
Gene: UROD
Database cross-references and differences (RAF-indexed):
Domains in SCOPe 2.08: d3gw3a_ - Heterogens: HOH
PDB Chain Sequences:
- Chain 'A':
Sequence, based on SEQRES records: (download)
>3gw3A (A:)
meanglgpqgfpelkndtflraawgeetdytpvwcmrqagrylpefretraaqdffstcr
speacceltlqplrrfpldaaiifsdilvvpqalgmevtmvpgkgpsfpeplreeqdler
lrdpevvaselgyvfqaitltrqrlagrvpligfagapwtlmtymvegggsstmaqakrw
lyqrpqashqllriltdalvpylvgqvvagaqalqlfeshaghlgpqlfnkfalpyirdv
akqvkarlreaglapvpmiifakdghfaleelaqagyevvgldwtvapkkarecvgntvt
lqgnldpcalyaseeeigqlvkqmlddfgphryianlghglypdmdpehvgafvdavhkh
srllrqn
Sequence, based on observed residues (ATOM records): (download)
>3gw3A (A:)
gfpelkndtflraawgeetdytpvwcmrqagrylpefretraaqdffstcrspeaccelt
lqplrrfpldaaiifsdilvvpqalgmevtmvpgkgpsfpeplreeqdlerlrdpevvas
elgyvfqaitltrqrlagrvpligfagapwtlmtymvegggsstmaqakrwlyqrpqash
qllriltdalvpylvgqvvagaqalqlfeshaghlgpqlfnkfalpyirdvakqvkarlr
eaglapvpmiifakdghfaleelaqagyevvgldwtvapkkarecvgntvtlqgnldpca
lyaseeeigqlvkqmlddfgphryianlghglypdmdpehvgafvdavhkhsrllrq