PDB entry 2v3d

View 2v3d on RCSB PDB site
Description: acid-beta-glucosidase with N-butyl-deoxynojirimycin
Class: hydrolase
Keywords: acid-beta-glucosidase, n-butyl-deoxynojirimycinalternative initiation, sphingolipid metabolism, gaucher disease, disease mutation, lipid metabolism, polymorphism, glycoprotein, pharmaceutical, n-butyl-deoxynojirimycin, alternative splicing, membrane, lysosome, hydrolase, glycosidase
Deposited on 2007-06-17, released 2007-08-14
The last revision prior to the SCOPe 2.08 freeze date was dated 2020-07-29, with a file datestamp of 2020-06-29.
Experiment type: XRAY
Resolution: 1.96 Å
R-factor: N/A
AEROSPACI score: 0.4 (click here for full SPACI score report)

Chains and heterogens:

  • Chain 'A':
    Compound: glucosylceramidase
    Species: Homo sapiens [TaxId:9606]
    Database cross-references and differences (RAF-indexed):
    • PDB 2V3D (499-End)
      • conflict (496)
    • Uniprot P04062 (2-498)
    Domains in SCOPe 2.08: d2v3da1, d2v3da2
  • Chain 'B':
    Compound: glucosylceramidase
    Species: Homo sapiens [TaxId:9606]
    Database cross-references and differences (RAF-indexed):
    • PDB 2V3D
      • conflict (496)
    • Uniprot P04062 (2-498)
    Domains in SCOPe 2.08: d2v3db1, d2v3db2
  • Heterogens: SO4, NBV, NAG, HOH

PDB Chain Sequences:

  • Chain 'A':
    Sequence, based on SEQRES records: (download)
    >2v3dA (A:)
    efarpcipksfgyssvvcvcnatycdsfdpptfpalgtfsryestrsgrrmelsmgpiqa
    nhtgtgllltlqpeqkfqkvkgfggamtdaaalnilalsppaqnlllksyfseegigyni
    irvpmascdfsirtytyadtpddfqlhnfslpeedtklkiplihralqlaqrpvsllasp
    wtsptwlktngavngkgslkgqpgdiyhqtwaryfvkfldayaehklqfwavtaenepsa
    gllsgypfqclgftpehqrdfiardlgptlansthhnvrllmlddqrlllphwakvvltd
    peaakyvhgiavhwyldflapakatlgethrlfpntmlfaseacvgskfweqsvrlgswd
    rgmqyshsiitnllyhvvgwtdwnlalnpeggpnwvrnfvdspiivditkdtfykqpmfy
    hlghfskfipegsqrvglvasqkndldavalmhpdgsavvvvlnrsskdvpltikdpavg
    fletispgysihtylwhrqllvdtm
    

    Sequence, based on observed residues (ATOM records): (download)
    >2v3dA (A:)
    efarpcipksfgyssvvcvcnatycdsfdpalgtfsryestrsgrrmelsmgpiqanhtg
    tgllltlqpeqkfqkvkgfggamtdaaalnilalsppaqnlllksyfseegigyniirvp
    mascdfsirtytyadtpddfqlhnfslpeedtklkiplihralqlaqrpvsllaspwtsp
    twlktngavngkgslkgqpgdiyhqtwaryfvkfldayaehklqfwavtaenepsaglls
    gypfqclgftpehqrdfiardlgptlansthhnvrllmlddqrlllphwakvvltdpeaa
    kyvhgiavhwyldflapakatlgethrlfpntmlfaseacvgskfweqsvrlgswdrgmq
    yshsiitnllyhvvgwtdwnlalnpeggpnwvrnfvdspiivditkdtfykqpmfyhlgh
    fskfipegsqrvglvasqkndldavalmhpdgsavvvvlnrsskdvpltikdpavgflet
    ispgysihtylwhrql
    

  • Chain 'B':
    Sequence, based on SEQRES records: (download)
    >2v3dB (B:)
    efarpcipksfgyssvvcvcnatycdsfdpptfpalgtfsryestrsgrrmelsmgpiqa
    nhtgtgllltlqpeqkfqkvkgfggamtdaaalnilalsppaqnlllksyfseegigyni
    irvpmascdfsirtytyadtpddfqlhnfslpeedtklkiplihralqlaqrpvsllasp
    wtsptwlktngavngkgslkgqpgdiyhqtwaryfvkfldayaehklqfwavtaenepsa
    gllsgypfqclgftpehqrdfiardlgptlansthhnvrllmlddqrlllphwakvvltd
    peaakyvhgiavhwyldflapakatlgethrlfpntmlfaseacvgskfweqsvrlgswd
    rgmqyshsiitnllyhvvgwtdwnlalnpeggpnwvrnfvdspiivditkdtfykqpmfy
    hlghfskfipegsqrvglvasqkndldavalmhpdgsavvvvlnrsskdvpltikdpavg
    fletispgysihtylwhrqllvdtm
    

    Sequence, based on observed residues (ATOM records): (download)
    >2v3dB (B:)
    arpcipksfgyssvvcvcnatycdsfdpptfpalgtfsryestrsgrrmelsmgpiqanh
    tgtgllltlqpeqkfqkvkgfggamtdaaalnilalsppaqnlllksyfseegigyniir
    vpmascdfsirtytyadtpddfqlhnfslpeedtklkiplihralqlaqrpvsllaspwt
    sptwlktngavngkgslkgqpgdiyhqtwaryfvkfldayaehklqfwavtaenepsagl
    lsgypfqclgftpehqrdfiardlgptlansthhnvrllmlddqrlllphwakvvltdpe
    aakyvhgiavhwyldflapakatlgethrlfpntmlfaseacvgskfweqsvrlgswdrg
    mqyshsiitnllyhvvgwtdwnlalnpeggpnwvrnfvdspiivditkdtfykqpmfyhl
    ghfskfipegsqrvglvasqkndldavalmhpdgsavvvvlnrsskdvpltikdpavgfl
    etispgysihtylwhrq